Table 1: Current International classification of EB.
Type Sub-type Target Proteins
EB simplex (EBS) Basal EBS Keratins 5 and 14; plectin; exofilin 5; 230 kd bullous pemphigoid antigen.
Suprabasal EBS Transglutaminase 5; Placofilina 1; desmoplachin; placoglobin
Junctional EB (JEB) Generalized JEB Laminin-332; Collagen XVII; integrin α6β4; integrin subunit α3
Localized JEB Laminin-332; Collagen XVII; integrin α6β4
Dystrophic EB Dominant EBD Collagen VII
Recessive EBD Collagen VII
Kindler’s Syndrome Kindlina-1